Sousa, F., Vicente, J., Azevedo, S., Pinto, A., Sousa, C. (2021). Darier´s disease as an unusual risk factor for otitis externa: A case report. Egyptian Journal of Ear, Nose, Throat and Allied Sciences, 22(22), 1-3. doi: 10.21608/ejentas.2020.50584.1284
Francisco Alves de Sousa; Joana Vicente; Sara Azevedo; Ana Nóbrega Pinto; Cecília Almeida Sousa. "Darier´s disease as an unusual risk factor for otitis externa: A case report". Egyptian Journal of Ear, Nose, Throat and Allied Sciences, 22, 22, 2021, 1-3. doi: 10.21608/ejentas.2020.50584.1284
Sousa, F., Vicente, J., Azevedo, S., Pinto, A., Sousa, C. (2021). 'Darier´s disease as an unusual risk factor for otitis externa: A case report', Egyptian Journal of Ear, Nose, Throat and Allied Sciences, 22(22), pp. 1-3. doi: 10.21608/ejentas.2020.50584.1284
Sousa, F., Vicente, J., Azevedo, S., Pinto, A., Sousa, C. Darier´s disease as an unusual risk factor for otitis externa: A case report. Egyptian Journal of Ear, Nose, Throat and Allied Sciences, 2021; 22(22): 1-3. doi: 10.21608/ejentas.2020.50584.1284
Darier´s disease as an unusual risk factor for otitis externa: A case report
1Departamento de Neurociências, Serviço de Otorrinolaringologia e Cirurgia Cérvico-Facial, Centro Hospitalar e Universitário do Porto, Porto, Portugal
2Serviço de Otorrinolaringologia e Cirurgia Cérvico-Facial, Centro Hospitalar e Universitário do Porto, Porto, Portugal
3Serviço de Otorrinolaringologia e Cirurgia Cérvico-Facial, Centro Hospitalar e Universitário do Porto, Porto, Portuga
4Diretora do Serviço de Otorrinolaringologia e Cirurgia Cérvico-Facial, Centro Hospitalar e Universitário do Porto, Porto, Portuga
Abstract
Background: Darier´s disease is known for affecting seborrheic areas of the body, including the ear, but no previous case reports describe recurrent otitis externa as a manifestation of this rare disease. Case presentation: We describe the case of a 70-year-old woman presenting to the Otolaryngology department with bilateral otalgia and pruritus with a 4-day evolution. She complained of recurrent similar episodes for many years requiring treatment. Scaly, pruritic, greasy lesions of the pinna were present and bilateral otitis externa was diagnosed. Inframammary and lower leg involuting lesions were also present. She had been diagnosed with Darier´s disease by the age of 16 years reporting frequent flares. Targeted treatment resolved the otologic complaints after 1 week and Dermatology evaluation was advised to pursue systemic medical optimization. Conclusion: Patients showing chronic otitis externa along with concurrent dermatologic lesions should be referred to the Dermatology clinic so that diagnostic investigation and targeted therapies may be offered.